Papillon‑Lefevre syndrome: Case series Vasumati I. Patel, Karan R. Thakkar, Shalini S. Gupta, Meghna J. Pujara Journal of Oral and Maxillofacial Pathology, 2024 Papillon-Lefevre syndrome (PLS) is an exceptional autosomal recessive disorder characterized by palmoplantar keratinization and premature loss of deciduous and permanent teeth. The palmoplantar keratoderma commonly has its onset between the ages of 1 and 4 years with severe periodontitis initiating at 3 or 4 years old. Parental consanguinity has been demonstrated in 20% to 40% of the cases. Management and preservation of teeth in such patients is a challenge to periodontists. Genetic studies have shown that mutation in the major gene locus of chromosome 11q14.1–q14.3 with the loss of function of the Cathepsin-C (CTSC) gene is responsible for PLS. An early diagnosis of the syndrome can help preserve the teeth through early institution of treatment, using a multidisciplinary approach. We hereby present four cases having all the characteristic features of the syndrome.
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Estimation and comparison of Serum C-reactive Protein Levels in Oral Sub mucous fibrosis and Oral Cancer: A Cross Sectional Study Hetul Patel, Hiren Patel, Bhupesh Patel, Priti Shah, Chirag Patel, Meghna Pujara Journal of Xidian University 19 (12), 730-742 , 2025 2025
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Estimation and correlation of α-amylase levels as salivary diagnostic biomarkers in smokeless tobacco users with periodontitis – A biochemical analysis. Pujara M, Gupta S, Patel V, Patel J Yugato 76 (1), 44-55 , 2024 2024
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MANAGEMENT OF ENDO-PERIO LESION USING CHORIONIC MEMBRANE AND CANCELLOUS BONE ALLOGRAFT: A CASE REPORT D Lathiya, V Patel, S Gupta, T Gangani, M Pujara, N Doshi Journal of Health Sciences 11 (1) , 2021 2021
A SURVEY ON THE USE OF ANTIBIOTICS AMONG THE DENTISTS IN GUJARAT V Patel, S Gupta, M Pujara, H Purani, V Pandya, T Gangani Journal of Health Sciences 10 (1) , 2020 2020
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